Hemorrhagic vasculitis hauv cov menyuam yaus

Cov me nyuam lub cev hemorrhagic vasculitis yog ib yam kab mob uas ua rau cov tawv nqaij tawv heev, nrog rau cov hlab ntsha ntawm cov hnyuv, cov pob yas qog thiab lub raum. Nws yog nyob rau hauv pab pawg neeg ntawm immunocomplex allergic vasopathies ntawm kis xwm. Qhov pib ntawm kev mob ntawm tus kab mob tuaj yeem tshwm sim thaum muaj hnub nyoog, tab sis, raws li txoj cai, me nyuam yaus (txog 3 xyoos) raug kev txom nyem los ntawm tus kab mob no tsis tshua muaj.

Feem ntau, vasculitis raug tshuaj ntsuam xyuas me nyuam yaus hnub nyoog 4 txog 12 xyoos.

Muaj ob peb hom mob hemorrhagic vasculitis, sib txawv hauv lawv qhov tshwm sim thiab qhov xwm txheej. Yog li, qhov vascopathy tau muab faib ua ob pawg: khub niam txiv (Hippel-Landau, Ehlers-Danlo syndrome, Casabaha-Merrita syndrome, Louis-Bar, etc.) thiab tau txais (symptomatic vasculitisitis los ntawm kev sib txawv ntawm ntau lub hauv paus pib, cov tshuaj lom, hypovitaminous thiab sib kis mob ntsws, lwm yam).

Vasculitis hemorrhagic: ua rau

Tus kab mob no yog tsim los ntawm kev puas tsuaj rau phab ntsa kab ntsig thiab nce nyob rau hauv cov kabmob ntawm cov hlab ntsha tag nrho, nrog rau kev sib xyaw ntawm kev sib txuam ua ke thiab nce hauv cov kab mob hauv lub cev.

Feem ntau, txoj kev loj hlob ntawm tus kab mob no pib qee zaus tom qab kis kab mob (ARVI, tonsillitis, liab plab, thiab lwm yam). Qee lub sij hawm txoj kev loj hlob ntawm vasculitis yog preceded by tshuaj tsis kam siv (lossis lwm yam kev fab tshuaj), hypothermia, txhaj tshuaj tiv thaiv, kev raug mob.

Cov tsos mob ntawm vasculitis hauv cov me nyuam

Hauv feem ntau tus neeg mob, feem ntau tshwm sim ntawm tus kab mob yog qhov tshwm sim ntawm daim tawv nqaij ntawm pob liab liab. Foci ntawm rashes: folds ntawm nquag, pob tw, ib cheeb tsam ib ncig ntawm lub pob yas qej txha. Tsis tshua pom tshwm ntsej muag rau ntawm lub ntsej muag, xib teg thiab taw, pob tw. Tom qab cov pob ua pob tom qab, me ntsis pigmented me ntsis nyob hauv nws qhov chaw, uas pib tev tawm nrog ntau zaus rov huam mob.

Cov tsos mob tshwm sim tom ntej no yog kev puas tsuaj. Nws tau pom los ntawm thawj lub lim tiam ntawm kev mob. Cov mob thiab qhov ntev ntawm qhov mob yuav txawv, feem ntau loj pob qij, tshwj xeeb tshaj yog pob taws thiab lub hauv caug, cuam tshuam. Nyob rau hauv rooj plaub no, cov pob txha ua ke, tab sis tsis muaj qhov deformations thiab cov nqaij ntshiv irreversible ntawm cov leeg.

Qhov teeb meem thib peb feem ntau yog mob plab. Ua tau manifest nrog los yog defeat lub tawv thiab pob qij txha. Kev mob ntawm kev mob tuaj yeem pheej rov ua dua txhua hnub, tsis muaj chaw nyob ruaj ntseg. Feem ntau, xeev siab, ntuav thiab kub cev kuj tau pom. Feem ntau, kev mob plab hnyuv los yog plab hnyuv los ntshav yuav ua tau.

Qee lub sij hawm nrog hemorrhagic vasculitis, lub raum lossis lwm yam plab hnyuv siab raum (lub ntsws, lub plawv, lub plawv, lub hlwb hlav) raug cuam tshuam. Qhov loj ntawm qhov txhab yuav ua tau ntau yam - los ntawm menyuam yaus, txog qee lub cev thiab mob hnyav.

Hemorrhagic vasculitis hauv cov menyuam: kev kho mob

Cov xwm txheej thiab cov hau kev ntawm txoj kev kho yuav txawv nyob ntawm seb lub sij hawm thiab daim ntawv ntawm tus kab mob (thawj zaug, rov qab kis ntawm tus kab mob los yog lub caij mus rau remission), ntawm qhov tshwm sim thiab mob hnyav, thiab nyob ntev thiab qhov xwm txheej ntawm tus kab mob. Tab sis nws yog tseem ua tau rau ib leeg tawm qhov feem ntau, hom kev kho mob.

Rau tag nrho cov ntaub ntawv ntawm tus kab mob, antiaggregants yog siv. Muab cov kabmob qhuav (persanthin, dipyridamole) 4 zaug ntawm ib hnub ntawm tus nqi ntawm 5-8 mg ib kilogram ntawm lub cev qhov hnyav, nrhiav (agapurine, pentoxifylline) 3 zaug ib hnub twg rau 5-10 mg / kg lub cev hnyav. Hauv cov mob hnyav, ob hom tshuaj muaj peev xwm ua tau rau tib lub sijhawm. Qhov ntev ntawm cov kev kho mob yuav txawv - ntawm 2 mus rau 12 lub hlis, nyob ntawm seb tus mob ntawm tus kab mob. Thaum daim ntawv ntev ntev xaiv cov hoob kawm ua ntu zus rov qab (quarterly lossis txhua txhua 6 lub hlis).

Cov txheej txheem siv tshuaj tua kab mob yog siv rau hauv tus neeg siv tshuaj, activators ntawm fibrinolysis, enterosorbents, glucocorticosteroids, membrane stabilizers, cytostatics, antihistamines. Transfusion therapy thiab plasmapheresis kuj tau siv. Kev xaiv ntawm kev siv yeeb siv tshuaj thiab txoj kev kho mob yuav tsum tau ua los ntawm tus kws kho mob, kev kho tus kheej lossis kev kho tsis tau kev tso cai ntawm kev kho mob yam tsis tau kev sab laj nrog cov kws tshwj xeeb thiab kev saib xyuas kev kho mob yog tsis tsim nyog.

Kev tiv thaiv ntawm hemorrhagic vasculitis

Qhov tseem ceeb tshaj plaws rau kev tiv thaiv ntawm tus kab mob yog kev tiv thaiv, kev tiv thaiv ntawm exacerbations ntawm kis foci, cais los ntawm allergens. Cov neeg mob tsis tuaj kuaj nrog cov kab mob antibens (Burne test, tuberculin, thiab lwm yam). Txhawm rau tiv thaiv kom tsis txhob muaj tus kab mob hemorrhagic vasculitis hauv cov menyuam yaus yog qhov tseem ceeb heev, kev noj zaubmov, kev noj zaubmov thiab kev noj qab nyob zoo.