Tus Fallot Notebook yog ib qho ntawm feem ntau lub plawv ntawm lub plawv uas muaj teeb meem hauv cov menyuam yaus (muaj npe rau tus kws kho mob Fabkis Phallo). Muaj plaub tug kev ua yuam kev, qhov muaj qhov tso cai rau koj mus tshawb nrhiav "tetralogy of Fallot":
- stenosis ntawm pulmonary artery - nqaim ntawm lub lumen ntawm pulmonary artery, uas ua rau txo tus nqi ntshav uas tau tso ntshav mus rau hauv cov ntsws, uas ua rau kev ua haujlwm ntawm txoj hlab ntsha;
- hypertrophy ntawm txoj hlab plawv (RV) - yog li qhov txiaj ntsig ntawm pulmonary artery stenosis, leeg nqaij ntawm prostate caj pas tuaj;
- Kev tiv thaiv ntawm kev kho hniav septum - muaj ib qho lumen ntawm txoj cai thiab sab laug voos (LV). Feem ntau, lawv raug sib cais los ntawm ib qho nqaij septum, vim muaj qhov sib txawv hauv qhov siab ntawm prostate thiab LV;
- dextrase ntawm aorta - lub tsho yog nyob rau sab xis ntawm lub plawv (nyob rau hauv lub cev - nyob rau sab laug).
Tetralogy ntawm Fallot - vim li cas
Yog vim li cas rau kev txhim kho ntawm kev sib haum xeeb ntawm Fallot, li cas los xij, zoo li lwm lub plawv dhia tsis meej - yog tsis paub. Muaj ntau yam kev tshawb fawb, kev tshwm sim ntawm kev taw qhia rau qhov kev sib txawv ntawm ntau hom kev sib txig.
Cov kws tshawb fawb tseem pom tias muaj cov kab mob hu ua MTHFR, muaj peev xwm ua rau tus me nyuam muaj kev puas tsuaj rau thaum lub nruab nrog cev (thaum lub sij hawm fetal).
Nws ntseeg tau hais tias mob qoob qhwv thiab lwm yam kab mob kis tau thaum lub sijhawm cev xeeb tub kuj tsis zoo rau kev tsim tawm ntawm lub plawv thiab cov hlab ntsha loj hauv lub fetus. Lwm Yam Uas Raug Tiv Thaiv Cov Tuag Fallo yog hnub nyoog ntawm leej niam (tshaj 40 xyoo), kev noj haus tsis zoo, haus dej cawv, haus luam yeeb, thiab ntshav qab zib ntawm leej niam.
Tsis tas li ntawd, nws raug sau tseg hais tias nyob rau hauv cov menyuam uas muaj tus mob Down syndrome, tetralogy ntawm Fallot yog ntau ntau dua rau cov me nyuam yaus.
Tetrada Fallot - kuaj mob
Cov tsos mob ntawm vps Tetrad Phallo yog raws li nram no:
- nyuaj rau kev pub mis rau menyuam;
- ncua kev loj hlob;
- cyanosis (cyanosis) ntawm daim tawv nqaij thaum quaj los yog pub mis;
- ua tsis taus pa thaum lub cev lub cev ua haujlwm (qhov ua rau muaj hnub nyoog).
Cov niam uas pom cov kev hloov hauv lawv cov me nyuam tig mus rau ib tus kws kho mob uas, raws li cov kev tshawb fawb nram qab no, tuaj yeem kuaj Tetrad Phallo:
- kev ntsuas ntshav;
- ntshav khov;
- echocardiography;
- Xoo hluav taws xob ntawm lub hauv siab (yog tias tom qab lo lus tawm ntawm lo lus nug);
- nuclear magnetic resonance (yog tias tus mob yog questionable);
- mob catheterization (hauv qee zaum tshwj xeeb).
Tetrada Fallot - kev kho mob
Cov menyuam yaus uas muaj asymptomatic tetralogy of Fallot tsis tas yuav tsum tau kev kho, tab sis yuav tsum tau soj ntsuam los ntawm ib tug kws kho plawv.
Kev kho ntawm kev sib daj sib deev ntawm Fallot hauv cov menyuam yaus uas muaj cov tsos mob ntawm cov tsos mob yog qhov tshwj xeeb phais. Txoj haujlwm zoo tshaj plaws thaum muaj hnub nyoog li ntawm 12 lub hlis (yog tias txoj kev tso cai).
Lub forecasts yog heev optimistic - feem ntau cov me nyuam tom qab kev cuam tshuam tau zoo heev ntawm kev ciaj sia taus thiab dab tsi ntau, lawv lub neej zoo siab.