Bullous pemphigoid

Bullous pemphigoid los yog Qib tus kab mob yog ib daim nqaij ntev ntawm cov tawv nqaij uas tsim muaj hlwv. Feem ntau, tus kab mob tshwm sim hauv cov neeg laus, hnub nyoog 60 xyoo thiab laus dua, tsis tshua muaj heev los ntawm tus kab mob Levera raug kev txom nyem me nyuam. Hauv qhov teeb meem no, cov pem hauv siab tau zoo heev, thiab cov duab thev naus laus zis muaj ntau yam nrog cov ncauj lus ua ke, uas qee yam mob nyhav thiab kho mob.

Cov tsos mob ntawm bullous pemphigoid

Feem ntau feem ntau tus kab mob cuam tshuam rau daim tawv nqaij ntawm lub cev thiab cov tawv nqaij, tsis tshua pom muaj cov pem hauv siab tau npog cov ntaub so ntswg ntawm lub taub hau, ntsej muag thiab cov npoo ntuj loj. Ib tug feature ntawm Lewra tus kab mob yog symmetrical eruptions, namely:

Lawv muaj cov kua ntshiab ntshiab, uas yog kev tiv thaiv los ntawm cov log tsheb nrig. Nws tsis yog tsis zoo rau ntawm daim tawv nqaij ntawm cov hlwv uas pom tshwm muaj xim zoo, tab sis feem ntau ntau pob ua ke nrog liab, uas yog ib qho kev qhia ntawm tus kab mob. Cov duab kos yog ntxiv los ntawm blisters ntawm ntau ntau thiab tsawg, uas tau erroneously qhia sarcoidosis.

Cov tsos mob tshwm sim yog thawj zaug thiab lawv tshwm sim rau thawj ob peb hnub, tom qab uas cov pob liab liab thiab cov hlwv qe yog qhib thiab tsim kev puas tsuaj hauv lawv qhov chaw. Nyob rau hauv cov ntaub ntawv ntawm bullous pemphigod, ulcers tsis them nrog crusts, tab sis epithelialized.

Nws tseem ceeb heev uas nyob rau hauv ib ntawm tsib tug neeg mob cov pob khaus feem ntau raug rau lub qhov ncauj thiab tsuas yog tshwm rau ntawm daim tawv nqaij.

Kev kho mob ntawm bullous pemphigoid

Lub peculiarity ntawm kev kho mob ntawm bullous pemphigoid los yog Qib tus kab mob yog nyob rau hauv qhov tseeb hais tias nws yuav tsum complex thiab ib tug neeg. Cov kws kho mob xaiv cov kev kho mob raws li cov lus qhia nram qab no:

Tab sis nyob rau hauv txhua rooj plaub, lub ntsiab lus tseem ceeb rau kev kho mob Qib tus kab mob yog cov tshuaj muaj glucocorticosteroids. Thaum pib ntawm kev kho mob, cov neeg mob tau sau 60-80 mg ntawm cov tshuaj hauv 24 xuab moos. Tom qab qhov no, tus kws kho mob, ua tus txheej txheem ntawm cov ntaub ntawv saum toj no, hloov cov tshuaj.

Kuj tseem ceeb rau kev kho mob ntawm pem hauv siab, immunosuppressants thiab cytostatics. Cov tshuaj no ua rau tsis muaj kev tiv thaiv, thiab tshem tawm cov qog. Nyob ntawm seb qhov kev mob tshwm sim loj npaum li cas thiab theem ntawm lawv txoj kev loj hlob, cov kev qhia muaj zog hauv lub cev yog cov tshuaj, cov tshuaj ua kom muaj cov khoom cog thiab cov tsiaj cov tsiaj uas ua rau muaj kev mob ntawm kev mob, kev ua haujlwm thiab kev tiv thaiv kab mob. Yog li, tus neeg mob tus mob zoo heev.