Behcet tus kab mob

Behcet tus kab mob yog ib hom kab mob ntsws mob heev, feem ntau cov kab mob hauv Nyiv thiab cov xeev Mediterranean. Feem ntau nws tshwm sim nyob rau hauv cov neeg laus hnub nyoog 30 - 40 xyoo. Tus kab mob no yog rau pawg neeg vasculitis thiab muaj ib qho kev tsis paub txog kev noj qab haus huv.

Ua rau Behcet tus mob

Txoj kev loj hlob ntawm tus kab mob no yog txuam nrog ntau yam tseem ceeb, xws li cov nram qab no:

Feem ntau cov kws txawj ntseeg hais tias qhov pib ntawm Behçet tus kab mob yog provoked los ntawm kis tus kab mob, thiab yav tom ntej, autoimmune mechanisms nrog rau lawv, muab cov tshuaj tiv thaiv kev xeeb tub.

Cov tsos mob ntawm Behcet tus kab mob rau cov poj niam

Tus kab mob no yog tus cwj pwm los ntawm polysimptomicity. Hauv qhov no, cov cim tseem ceeb, uas koj tuaj yeem ua tau kom paub tseeb, yog txuam nrog kev puas tsuaj rau lub qhov ncauj ntawm qhov ncauj thiab cov qoob loo, nrog rau kev ua rau lub qhov muag. Xav txog tag nrho cov manifestations Behçet tus kab mob nyob rau hauv ntau yam.

Kab noj hniav puas tsuaj

Pib, cov hlwv me me nrog cov pos huab tshwm tuaj rau ntawm daim di ncauj, ntuj, nplaig, pos hniav, pharynx, puab sab hauv puab tsaig, uas yog tom qab qhib. Nyob rau hauv qhov chaw ntawm vesicles, puag ncig, mob nplooj (aphthae) ntawm ci xim liab yog tsim, qhov loj ntawm uas muaj peev xwm ncav cuag 2 cm nyob rau hauv lub cheeb. Qhov kho ntawm qhov tshwm sim tshwm sim txog ib lub hlis tom qab, nrog 3-4 zaus hauv ib lub xyoo cov lesion recurs.

Qhov chaw mob qhov chaw mos

Cov poj niam nyob rau hauv daim nyias nyias ntawm qhov chaw mos thiab qhov nqaij mos, muaj mob heev, zoo ib yam li cov uas tshwm hauv lub qhov ncauj. Tom qab kho, cov nti tau nyob hauv lawv qhov chaw.

Kev puas tsuaj ntawm qhov tsis pom kev

Cov kev tshwm sim tshwm sim li ob peb lub lis piam tom qab cov tsos mob nyob hauv lub qhov ncauj kab noj hniav. Cov neeg tuaj yeem tuaj yeem tsim muaj mob ntawm lub plawv iris thiab ciliary ntawm lub qhov muag, qhov mob ntawm cov vascular thiab mucous daim nyias nyias ntawm lub qhov muag, qhov mob ntawm lub qhov ntsej muag. Feem ntau muaj cov tsos mob nram no: photophobia, qhov muag tsis pom kev, lacrimation ntau dua.

Cov kab mob ntshav liab

Nodular erythema, pyoderma, pashulo-vesicular pob yog tawm. Kuj qee zaum, zes plaub hau poob, subungual panaritium tau pom.

Kev puas tsuaj ntawm tus mob musculoskeletal

Muaj kev mob ntawm kev mob caj dab (feem ntau sab qis dua) uas tsis muaj kev puas tsuaj.

Cov tsos mob neurological

Muaj phenomena ntawm cranial hlab ntsha kev puas tsuaj, txoj kev loj hlob ntawm meningoencephalitis, edema ntawm cov hlab ntsha optic, cov tsos mob ntawm hemiparesis.

Intravascular inflammatory hloov

Yam ntxwv ntawm kev loj hlob ntawm vasculitis, thrombophlebitis ntawm veins rau ntawm ob txhais ceg, thrombosis ntawm hepatic leeg thiab thromboembolism ntawm pulmonary artery, aortic aneurysm, thiab lwm yam.

Nrog rau qhov chaw ntawm cov mob plab, lub plawv thiab lub ntsws, muaj xws li cov tsos mob xws li:

Kev kho mob ntawm Behcet tus mob

Kev kho mob ntawm Behcet tus kab mob, ua ntej ntawm tag nrho, yog tsom rau maximizing tus neeg mob lub neej, ua tiav ib lub caij ntev remission thiab tiv thaiv kev hloov tsis tau nyob rau hauv lub nruab nrog cev.

Cov hlab ntsha ntawm Behcet's syndrome nyob hauv lub qhov ncauj thiab cov qog nqaij hlav yuav raug nyob hauv kev kho mob hauv zos nrog kev siv glucocorticosteroids , tshuaj tiv thaiv antiseptic, thiab qee zaus - cov tshuaj antipodal. Tsis tas li ntawd rau kev kho mob ntawm tus kab mob, cytostatic cov neeg ua hauj lawm, immunosuppressors, cov vitamins yuav qhia. Kab mob vascular raug kho los ntawm txoj kev phais mob. Ntau tus neeg mob yog cov tshuaj tua kab mob hauv cov tshuaj hu ua extracorporal hemocorrection. Kev kho yog ua tiav nyob rau hauv kev kho mob tas li.